KLIPPEL - TRENAUNAY SYNDROME IN COMBINATION WITH OVARIAN CANCER
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Keywords

Klippel-Trenaunay syndrome, ovarian cancer, angiodysplasia, express histology

Abstract

The article presents a clinical case of ovarian cancer, which was diagnosed in a patient with Klippel-Trenaunay syndrome. The clinical picture of the disease was dominated by pain and an increase in the size of the abdomen, urinary retention and stool, severe general weakness, malaise, and palpitations. After a diagnostic examination and preliminary preparation, the patient was operated on for health reasons in a hospital at the oncogynecology department of the Tashkent City branch of the Republican Specialized Scientific and Practical Medical Center of Oncology and Radiology with a preliminary diagnosis of an ovarian tumor. Interrooperatively, revealed angiodysplastic changes in the vessels of the internal organs, and the nature of the ovarian tumor, G2 adenocarcinoma, was also clarified. This clinical case is a unique example of a combination of congenital angiodysplasia syndrome and ovarian cancer. These data may help in the management of patients with this pathology and improve the survival rate of patients with Klippel-Trenaunay syndrome.

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